Laparoscopicbiopsy-provenlupusnephritisinautosomaldominant polycystic kidneydisease

  • 박지인
  • 김성권
  • 진호준

초록

A 48-year-oldwomanwithautosomaldominantpolycystickidneydisease(ADPKD)presentedwithgeneralizededemaandarthralgia.Sheshowedevidencesofacute glomerulonephritisincludingnephrotic-rangedproteinuria.Becauseherserologic testresultswereconsistentwiththoseforsystemiclupuserythematosus(SLE),we performedlaparoscopicrenalbiopsythatconfirmedWorldHealthOrganization (WHO)classIVlupusnephritis.Shewastreatedwithsteroidsandintravenous cyclophosphamidepulsetherapyandeventuallystartedhemodialysis8yearsafter thelupusnephritiswasdiagnosed.Toourknowledge,thisisthefirstcasewhereina patientwithADPKDunderwentalaparoscopicbiopsyfordiagnosinglupusnephritis.

키워드

Laparoscopy Lupus nephritis Polycystic kidneydisease
제목
Laparoscopicbiopsy-provenlupusnephritisinautosomaldominant polycystic kidneydisease
저자
박지인김성권진호준
발행일
2012-09
유형
Y
저널명
Kidney Research and Clinical Practice
31
3
페이지
192 ~ 195