Wegener's Granulomatosis Presenting as Pyoderma Gangrenosum

괴저농피증으로 발현한 베게너 육아종증 1예
  • 남승주
  • 우진현
  • 최성재
  • 지종대
  • 송관규
  • 외 1명

초록

Wegener’s granulomatosis is multi-systemic disease characterized by granulomatous necrotizing vasculitis and it usually affects upper and lower respiratory tracts. Cutaneous manifestation as an initial presentation is unusual and comprises about 15% of cases. The most frequent skin lesions are palpable purpura, papules, ulcerations, vesicles, subcutaneous nodules, necrotizing ulcerations. We report a patient with Wegener’s granulomatosis who presents as a pyoderma gangrenosum.

키워드

Wegener granulomatosisPyoderma gangrenosumSkin Manifestations
제목
Wegener's Granulomatosis Presenting as Pyoderma Gangrenosum
제목 (타언어)
괴저농피증으로 발현한 베게너 육아종증 1예
저자
남승주우진현최성재지종대송관규이영호
발행일
2008-06
유형
Y
저널명
대한류마티스학회지
15
2
페이지
153 ~ 158